Which of the following activate adenylyl cyclase?

Which of the following activates hormone sensitive lipase?

Order the steps of lipid metabolism.

Which of the following encourages lipogenesis?

Which of the following are ketone bodies?

What is arachidonic acid the precursor to?

Match the compound and its functions.

Which of the following inhibits HMG-CoA reductase?

What makes up sphingomyelin?

Which of the following is a deficiency of sphingomyelinase?

Which of the following is a deficiency of alpha-glucosidase?

Which of the following is a deficiency of beta-galactosidase?

Which of the following is a deficiency of aryl sulfatase?

Which of the following is a deficiency of alpha-galactosidase?

Which of the following is a deficiency of hexosaminidase?

A pt who is an Ashkenazi Jew presents with cherry red macula, ID, and blindness. Which of the following conditions do they have?

A pt presents with cherry red macula, ID, hepatomegaly, and splenomegaly. Which of the following conditions do they have?

A pt who is an Ashkenazi Jew presents with hepatomegaly, ID, splenomegaly and erosion of long bones (osteoporosis). Which of the following conditions do they have?

A pt presents with ID, deafness, convulsions, paralysis, and blindness. Which of the following conditions do they have?

A pt presents with angiokeratomas, reddish-purple rash, kidney failure, and heart failure. Which of the following conditions do they have?

A pt presents with ID, psych problems, dementia, and progressive paralysis. Which of the following conditions do they have?

Which of the following cleaves part of arginine and lysine?

Which of the following cleaves part of tyrosine, phenylalanine, tryptophan, and leucine?

Which of the following are products of tyrosine metabolism?

Which of the following are products of tryptophan metabolism?

Which of the following are products of glutamate metabolism?

Which of the following are products of glycine metabolism?

Match the enzyme disorders and their deficiencies.

A pt presents with unpigmented eyes, skin and hair. You determine them to be at increased risk of melanoma, squamous cell CA, and actinic keratosis. What condition do they have?

A pt presents with musty odor urine, hypopigmentation, and ID. What condition do they have?

A pt presents with degenerative arthritis, darkly pigmented urine when exposed to air, and pigmentation of CT. What condition do they have?

A pt presents with urine that smells like burnt sugar, weakness, and brain damage leading to ID. What condition do they have?

A pt presents with ID, increased CAD, and increased platelet aggregation and endothelial damage. What condition do they have?

Which of the following is due to a defect in membrane transport of cysteine, ornithine, arginine, and lysine?

Which of the following is due to a defect in membrane transport of tryptophan?

Which of the following is characterized by a increased Km and same Vmax?

Which of the following is characterized by a decreased Vmax and same Km?

Sort the characteristics.

Match the defect and disease.

Match the glycogen storage diseases and their defects.

Match the glycogen storage diseases and their effect.

A pt presents with corneal clouding and intellectual disability with myocardial ischemia, coarse facial features, and dwarfing. What do they have?

A pt presents with corneal clouding, NL intelligence, aortic valve disease and stiff joints. What do they have?

A pt presents with intellectual disability, coarse facial features, neuro problems, thickened myocardium, and short stature. What do they have?

Match the defect and condition.

What B vitamins belong in which category.

Match the sx to vitamin deficiency.

What enzymes in gluconeogenesis are inhibited by insulin?

What stimulates gluconeogenesis?

Match the drug and what it inhibits.

Which of the following are effects of insulin on fat?

What are the main effects of glucagon on fat?

What are the effects of GH on fat?

What are the effects of cortisol on fat?

What is the effect of insulin on carbs/sugar?

What is the effect of glucagon on carbs/sugar?

What is the effect of GH on carbs/sugar?

What is the effect of cortisol on carbs/sugar?

What is the effect of insulin on protein?

What is the effect of glucagon on protein?

What is the effect of GH on protein?

What is the effect of cortisol on protein?

What is characteristic in each compartment?